Abstract

Craniosynostosis is the pre- or perinatal premature fusion of one or more cranial sutures that results in abnormal calvarial shape and cranial growth patterns. The features of cranial shape are specific for each type of suture fusion.

Craniosynostosis is one of the most common craniofacial malformations besides cleft-lip and palate.

In most craniosynostosis cases only one suture is fused and in these cases the etiology is not always known. Multiple suture synostosis is usual ly associated with a syndromic disease. If uncorrected, craniosynostosis might result in increased intracranial pressure (ICP), which can occur even in absence of clinical signs.

It is extremely important to diagnose craniosynostosis in a very early stage to prevent any possible brain damage and permanent craniofacial deformation. All children with suspected craniosynostosis should be referred to a specialist for the confirmation of diagnosis and for development of a careful treatment plan.